ARPKD
Hepatic cysts leads to portal HTN and cholangitisEnlarged kidneys –> No amniotic fluids –> Pulmonary hypoplasia –> Pulmonary insufficiency
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ARPKD
Hepatic cysts leads to portal HTN and cholangitisEnlarged kidneys –> No amniotic fluids –> Pulmonary hypoplasia –> Pulmonary insufficiency