Systemic scleroderma s/s,”Systemic: fatigue, joint stiffness/ pain Skin: telangiectasia, sclerodactyly, digital ulcers, calcinosis cutis Vascular: raynaud GI: dysphagia, dyspepsia, angiodysplasia, malabsorption Pulm: pulm fibrosis, pulm arterial HTNRenal: crisis: acute oliguric renal failure + malig HTN, thrombocytopenia, MAHACardiac: myocarditis, pericardidits
pericardial effusion + ANA and + anti-topo-I-ab”